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  • Dumlupınar Üniversitesi Fen Bilimleri Enstitüsü Dergisi
  • Issue:014
  • A CASE WITH WOLFRAM (DIDMOAD) SYNDROME AND ORAL FINDINGS (A CASE REPORT)

A CASE WITH WOLFRAM (DIDMOAD) SYNDROME AND ORAL FINDINGS (A CASE REPORT)

Authors : Hasan HATİPOĞLU, Müjgan Güngör HATİPOĞLU, Özden KANSU
Pages : 137-140
View : 20 | Download : 12
Publication Date : 2007-12-17
Article Type : Research Paper
Abstract :Wolfram Sendromu, nadir görülen konjenital, birçok sistemi etkileyebilen sendromdur. Diabetes mellitus, diabetes insipidus, optik atrofi ve sağırlık ile karakterizedir. Hastalarda nörolojik rahatsızlıklar ile üriner sistem rahatsızlıkları ve psikolojik rahatsızlıklar da izlenir. Diabetes mellitus ve optik atrofi ilk ortaya çıkan bulgulardır. Bu olgu raporunda 20 yaşındaki Wolfram sendromlu erkek hastanın klinik ve radyografik ağız bulguları sunulmaktadır.
Keywords : Wolfram sendromu, DIDMOAD, oral bulgular

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