Adenoid Cystic Carcinoma of Vulva: Case Report

Authors : Terrab FATİMA ZAHRAE, Rajae ENNOUİCHİ, Fadoua ALLOUCHE, Zenab ALAMİ, Touria BOUHAFA, Khalid HASSOUNİ

Pages : 53-56

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Publication Date : 2019-12-01

Article Type : Other Papers

Abstract :The adenoid cystic carcinoma insert ignore into journalissuearticles values(ACC); of the Bartholin’s gland insert ignore into journalissuearticles values(BG); is one of the most  uncommon variant of vulvar malignancies representing only 10–15% of cases. Risk  factors to the development of ACCBG are still unclear. The symptoms are usually  non-specific .  In the present study, we present a 61-year-old woman with a vulvar mass evolving  since 4 years, without pruritus or pains, without other signs. She initially benefited of  an excisional biopsy of the mass returning in favour of a nodular hidradenoma. The  evolution after 1 year was marked by the recurrence of the mass, the patient had an  ablation of the masse then a total vulvectomy and bilateral lymph node dissection  because pathology showed ACC of Bartholin’s gland with positif surgical margins.  She received adjuvant external beam radiation to the pelvis and on the operating  bed. Patient’s evolution was marked by complete remission maintained after 4years  follow-up. Conclusion : Adenoid cystic carcinoma of vulva is an extremely rare, slowly  progressing neoplasm mostly involving the Bartholin’s gland. The usual treatment  includes wide excision and adjuvant radiotherapy insert ignore into journalissuearticles values(if required);. There may be late  local and distant recurrence.
Keywords : adenoid cystic carcinoma, bartholin`s gland, surgery, radiotherapy, chemotherapy, surhical margins